An extremely rare presentation of extrapulmonary involvement of inflammatory myofibroblastic tumour of small intestine causing intussusception

Inflammatory myofibroblastic tumour (IMFT) is an uncommon mesenchymal solid tumour commonly documented in children and young adults. It is usually located in lungs however; extrapulmonary involvement has also been reported. IMFT of the small bowel is rare and to our knowledge, only 27 cases have been reported to date in the literature under several names worldwide. Here we report a 28th case of IMFT in a 62 year old man presenting as an ileoileal intussusception. Intussusception in adults presents with non-specific symptoms and classical image signs facilitate preoperative diagnosis. IMFT diagnosis is histopathological which usually implies surgical resection. IMFT must be kept in mind in the differential diagnosis of malignant spindle cell tumours of the small bowel. Immunohistochemical stains are essential for accurate diagnosis. Complete surgical excision, with microscopically clear margins is the mainstay of treatment.