Dyke -davidoff-masson syndrome: A rare case report

Dyke-Davidoff-Masson Syndrome (DDMS)also known as cerebral hemiatrophy is a rare neurological disease characterized by Seizures, hemiparesis, cerebral hemiatrophy, facial and body asymmetry with mild intellectual disability. DDMS can be diagnosed by characterized by classical radiographical findings, that is cerebral hemiatrophy, ipsilateral dilated ventricle, ipsilateral osseus hypertrophy and excessive pneumatization of ipsilateral frontal and other sinuses. DDMS presents withearlypartial onset seizure with hemiparesis. Later in adolescence facial and body asymmetry is evident with mild cognitive dysfunction. We are presenting a case in which a23 year oldmale presented with uncontrolled partial onset seizures with secondary generalization, right hemiparesis, right sided hemiatrophy of limbs and body with characteristic radiological findings suggestive of DDMS.